Contrasting Outcomes in Two Cases of Uterine PEComa

Abstract Perivascular epithelioid cell tumours of the uterus are rare neoplasms with only few cases described in literature. Ongoing contribution to literature is important order understand natural history for diagnosis and management challenges PEComa. We present two contrasting PEComa who presented postmenopausal bleeding, were diagnosed on endometrial biopsy had surgical treatment. The first patient following treatment has been disease free four years while regular follow-ups. second aggressive developed early recurrence requiring chemotherapy died 17 months from diagnosis. a tumour usually good outcomes, where surgery itself adequate There not much evidence available currently use cases, such as our case, presents aggressively. In this article, we elaborate outcomes one presentation being chemotherapy. evaluated current cases.